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National experience with adenosine deaminase deficiency related SCID in Polish children.
Dąbrowska-Leonik N, Piątosa B, Słomińska E, Bohynikova N, Bernat-Sitarz K, Bernatowska E, Wolska-Kuśnierz B, Kałwak K, Kołtan S, Dąbrowska A, Goździk J, Ussowicz M, Pac M. Dąbrowska-Leonik N, et al. Among authors: wolska kusnierz b. Front Immunol. 2023 Jan 6;13:1058623. doi: 10.3389/fimmu.2022.1058623. eCollection 2022. Front Immunol. 2023. PMID: 36685585 Free PMC article.
BCG Moreau Vaccine Safety Profile and NK Cells-Double Protection Against Disseminated BCG Infection in Retrospective Study of BCG Vaccination in 52 Polish Children with Severe Combined Immunodeficiency.
Bernatowska E, Skomska-Pawliszak M, Wolska-Kuśnierz B, Pac M, Heropolitanska-Pliszka E, Pietrucha B, Bernat-Sitarz K, Dąbrowska-Leonik N, Bohynikova N, Piątosa B, Lutyńska A, Augustynowicz E, Augustynowicz-Kopeć E, Korzeniewska-Koseła M, Krasińska M, Krzysztopa-Grzybowska K, Wieteska-Klimczak A, Książyk J, Jackowska T, van den Burg M, van Dongen JJM, Casanova JL, Picard C, Mikołuć B. Bernatowska E, et al. J Clin Immunol. 2020 Jan;40(1):138-146. doi: 10.1007/s10875-019-00709-1. Epub 2019 Nov 20. J Clin Immunol. 2020. PMID: 31749033 Free PMC article.
COVID-19 in unvaccinated patients with inborn errors of immunity-polish experience.
Kołtan S, Ziętkiewicz M, Grześk E, Becht R, Berdej-Szczot E, Cienkusz M, Ewertowska M, Heropolitańska-Pliszka E, Krysiak N, Lewandowicz-Uszyńska A, Mach-Tomalska M, Matyja-Bednarczyk A, Milchert M, Napiórkowska-Baran K, Pieniawska-Śmiech K, Pituch-Noworolska A, Renke J, Roliński J, Rywczak I, Stelmach-Gołdyś A, Strach M, Suchanek H, Sulicka-Grodzicka J, Szczawińska-Popłonyk A, Tokarski S, Więsik-Szewczyk E, Wolska-Kuśnierz B, Zeman K, Pac M. Kołtan S, et al. Among authors: wolska kusnierz b. Front Immunol. 2022 Sep 23;13:953700. doi: 10.3389/fimmu.2022.953700. eCollection 2022. Front Immunol. 2022. PMID: 36211407 Free PMC article.
Common variable immune deficiency in children--clinical characteristics varies depending on defect in peripheral B cell maturation.
Piątosa B, Pac M, Siewiera K, Pietrucha B, Klaudel-Dreszler M, Heropolitańska-Pliszka E, Wolska-Kuśnierz B, Dmeńska H, Gregorek H, Sokolnicka I, Rękawek A, Tkaczyk K, Bernatowska E. Piątosa B, et al. J Clin Immunol. 2013 May;33(4):731-41. doi: 10.1007/s10875-013-9875-4. Epub 2013 Feb 7. J Clin Immunol. 2013. PMID: 23389235 Free PMC article.
Nijmegen Breakage Syndrome: Clinical and Immunological Features, Long-Term Outcome and Treatment Options - a Retrospective Analysis.
Wolska-Kuśnierz B, Gregorek H, Chrzanowska K, Piątosa B, Pietrucha B, Heropolitańska-Pliszka E, Pac M, Klaudel-Dreszler M, Kostyuchenko L, Pasic S, Marodi L, Belohradsky BH, Čižnár P, Shcherbina A, Kilic SS, Baumann U, Seidel MG, Gennery AR, Syczewska M, Mikołuć B, Kałwak K, Styczyński J, Pieczonka A, Drabko K, Wakulińska A, Gathmann B, Albert MH, Skarżyńska U, Bernatowska E; Inborn Errors Working Party of the Society for European Blood and Marrow Transplantation and the European Society for Immune Deficiencies. Wolska-Kuśnierz B, et al. J Clin Immunol. 2015 Aug;35(6):538-49. doi: 10.1007/s10875-015-0186-9. Epub 2015 Aug 14. J Clin Immunol. 2015. PMID: 26271390
EuroFlow Standardized Approach to Diagnostic Immunopheneotyping of Severe PID in Newborns and Young Children.
Kalina T, Bakardjieva M, Blom M, Perez-Andres M, Barendregt B, Kanderová V, Bonroy C, Philippé J, Blanco E, Pico-Knijnenburg I, Paping JHMP, Wolska-Kuśnierz B, Pac M, Tkazcyk J, Haerynck F, Akar HH, Formánková R, Freiberger T, Svatoň M, Šedivá A, Arriba-Méndez S, Orfao A, van Dongen JJM, van der Burg M. Kalina T, et al. Front Immunol. 2020 Mar 19;11:371. doi: 10.3389/fimmu.2020.00371. eCollection 2020. Front Immunol. 2020. PMID: 32265901 Free PMC article.
The Clinical and Genetic Spectrum of 82 Patients With RAG Deficiency Including a c.256_257delAA Founder Variant in Slavic Countries.
Sharapova SO, Skomska-Pawliszak M, Rodina YA, Wolska-Kuśnierz B, Dabrowska-Leonik N, Mikołuć B, Pashchenko OE, Pasic S, Freiberger T, Milota T, Formánková R, Szaflarska A, Siedlar M, Avčin T, Markelj G, Ciznar P, Kalwak K, Kołtan S, Jackowska T, Drabko K, Gagro A, Pac M, Naumova E, Kandilarova S, Babol-Pokora K, Varabyou DS, Barendregt BH, Raykina EV, Varlamova TV, Pavlova AV, Grombirikova H, Debeljak M, Mersiyanova IV, Bondarenko AV, Chernyshova LI, Kostyuchenko LV, Guseva MN, Rascon J, Muleviciene A, Preiksaitiene E, Geier CB, Leiss-Piller A, Yamazaki Y, Kawai T, Walter JE, Kondratenko IV, Šedivá A, van der Burg M, Kuzmenko NB, Notarangelo LD, Bernatowska E, Aleinikova OV. Sharapova SO, et al. Front Immunol. 2020 Jun 10;11:900. doi: 10.3389/fimmu.2020.00900. eCollection 2020. Front Immunol. 2020. PMID: 32655540 Free PMC article.
49 results