Starost MF - Search Results

1

Liver-directed gene therapy for murine glycogen storage disease type Ib.

Kwon JH, Lee YM, Cho JH, Kim GY, Anduaga J, Starost MF, Mansfield BC, Chou JY. Kwon JH, et al. Among authors: starost mf. Hum Mol Genet. 2017 Nov 15;26(22):4395-4405. doi: 10.1093/hmg/ddx325. Hum Mol Genet. 2017. PMID: 28973635 Free PMC article.

2

Angiotensin mediates renal fibrosis in the nephropathy of glycogen storage disease type Ia.

Yiu WH, Pan CJ, Ruef RA, Peng WT, Starost MF, Mansfield BC, Chou JY. Yiu WH, et al. Among authors: starost mf. Kidney Int. 2008 Mar;73(6):716-23. doi: 10.1038/sj.ki.5002718. Epub 2007 Dec 12. Kidney Int. 2008. PMID: 18075499 Free PMC article.

3

Necrotic foci, elevated chemokines and infiltrating neutrophils in the liver of glycogen storage disease type Ia.

Kim SY, Weinstein DA, Starost MF, Mansfield BC, Chou JY. Kim SY, et al. Among authors: starost mf. J Hepatol. 2008 Mar;48(3):479-85. doi: 10.1016/j.jhep.2007.11.014. Epub 2007 Dec 28. J Hepatol. 2008. PMID: 18191274 Free PMC article.

4

Normoglycemia alone is insufficient to prevent long-term complications of hepatocellular adenoma in glycogen storage disease type Ib mice.

Yiu WH, Pan CJ, Mead PA, Starost MF, Mansfield BC, Chou JY. Yiu WH, et al. Among authors: starost mf. J Hepatol. 2009 Nov;51(5):909-17. doi: 10.1016/j.jhep.2008.11.026. Epub 2009 Feb 5. J Hepatol. 2009. PMID: 19376605 Free PMC article.

5

Mouse Prkar1a haploinsufficiency leads to an increase in tumors in the Trp53+/- or Rb1+/- backgrounds and chemically induced skin papillomas by dysregulation of the cell cycle and Wnt signaling.

Almeida MQ, Muchow M, Boikos S, Bauer AJ, Griffin KJ, Tsang KM, Cheadle C, Watkins T, Wen F, Starost MF, Bossis I, Nesterova M, Stratakis CA. Almeida MQ, et al. Among authors: starost mf. Hum Mol Genet. 2010 Apr 15;19(8):1387-98. doi: 10.1093/hmg/ddq014. Epub 2010 Jan 15. Hum Mol Genet. 2010. PMID: 20080939 Free PMC article.

6

Haploinsufficiency for either one of the type-II regulatory subunits of protein kinase A improves the bone phenotype of Prkar1a+/- mice.

Liu S, Saloustros E, Mertz EL, Tsang K, Starost MF, Salpea P, Faucz FR, Szarek E, Nesterova M, Leikin S, Stratakis CA. Liu S, et al. Among authors: starost mf. Hum Mol Genet. 2015 Nov 1;24(21):6080-92. doi: 10.1093/hmg/ddv320. Epub 2015 Aug 5. Hum Mol Genet. 2015. PMID: 26246497 Free PMC article.

7

Glycogen storage disease type Ia mice with less than 2% of normal hepatic glucose-6-phosphatase-α activity restored are at risk of developing hepatic tumors.

Kim GY, Lee YM, Kwon JH, Cho JH, Pan CJ, Starost MF, Mansfield BC, Chou JY. Kim GY, et al. Among authors: starost mf. Mol Genet Metab. 2017 Mar;120(3):229-234. doi: 10.1016/j.ymgme.2017.01.003. Epub 2017 Jan 10. Mol Genet Metab. 2017. PMID: 28096054 Free PMC article.

8

Gene therapy prevents hepatic tumor initiation in murine glycogen storage disease type Ia at the tumor-developing stage.

Cho JH, Lee YM, Starost MF, Mansfield BC, Chou JY. Cho JH, et al. Among authors: starost mf. J Inherit Metab Dis. 2019 May;42(3):459-469. doi: 10.1002/jimd.12056. Epub 2019 Mar 6. J Inherit Metab Dis. 2019. PMID: 30637773 Free PMC article.

9

Gene therapy using a novel G6PC-S298C variant enhances the long-term efficacy for treating glycogen storage disease type Ia.

Zhang L, Lee C, Arnaoutova I, Anduaga J, Starost MF, Mansfield BC, Chou JY. Zhang L, et al. Among authors: starost mf. Biochem Biophys Res Commun. 2020 Jun 30;527(3):824-830. doi: 10.1016/j.bbrc.2020.04.124. Epub 2020 May 16. Biochem Biophys Res Commun. 2020. PMID: 32430177 Free PMC article.

10

Prkar1a haploinsufficiency ameliorates the growth hormone excess phenotype in Aip-deficient mice.

Schernthaner-Reiter MH, Trivellin G, Roetzer T, Hainfellner JA, Starost MF, Stratakis CA. Schernthaner-Reiter MH, et al. Among authors: starost mf. Hum Mol Genet. 2020 Oct 10;29(17):2951-2961. doi: 10.1093/hmg/ddaa178. Hum Mol Genet. 2020. PMID: 32821937 Free PMC article.

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