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The Effect of Various Doses of Phenylalanine Supplementation on Blood Phenylalanine and Tyrosine Concentrations in Tyrosinemia Type 1 Patients.
Nutrients. 2019 Nov 18;11(11):2816. doi: 10.3390/nu11112816.
Nutrients. 2019.
PMID: 31752110
Free PMC article.
Daily variation of NTBC and its relation to succinylacetone in tyrosinemia type 1 patients comparing a single dose to two doses a day.
Kienstra NS, van Reemst HE, van Ginkel WG, Daly A, van Dam E, MacDonald A, Burgerhof JGM, de Blaauw P, McKiernan PJ, Heiner-Fokkema MR, van Spronsen FJ.
Kienstra NS, et al.
J Inherit Metab Dis. 2018 Mar;41(2):181-186. doi: 10.1007/s10545-017-0112-9. Epub 2017 Nov 23.
J Inherit Metab Dis. 2018.
PMID: 29170874
Free PMC article.
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