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IGF-1:tetanus toxin fragment C fusion protein improves delivery of IGF-1 to spinal cord but fails to prolong survival of ALS mice.
Brain Res. 2009 Sep 1;1287:1-19. doi: 10.1016/j.brainres.2009.06.066. Epub 2009 Jun 27.
Brain Res. 2009.
PMID: 19563785
Tetanus toxin fragment C fusion facilitates protein delivery to CNS neurons from cerebrospinal fluid in mice.
Benn SC, Ay I, Bastia E, Chian RJ, Celia SA, Pepinsky RB, Fishman PS, Brown RH Jr, Francis JW.
Benn SC, et al. Among authors: chian rj.
J Neurochem. 2005 Nov;95(4):1118-31. doi: 10.1111/j.1471-4159.2005.03459.x.
J Neurochem. 2005.
PMID: 16271047
Free article.
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A glial cell line-derived neurotrophic factor (GDNF):tetanus toxin fragment C protein conjugate improves delivery of GDNF to spinal cord motor neurons in mice.
Larsen KE, Benn SC, Ay I, Chian RJ, Celia SA, Remington MP, Bejarano M, Liu M, Ross J, Carmillo P, Sah D, Phillips KA, Sulzer D, Pepinsky RB, Fishman PS, Brown RH Jr, Francis JW.
Larsen KE, et al. Among authors: chian rj.
Brain Res. 2006 Nov 20;1120(1):1-12. doi: 10.1016/j.brainres.2006.08.079. Epub 2006 Oct 3.
Brain Res. 2006.
PMID: 17020749
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Recombinant GDNF: tetanus toxin fragment C fusion protein produced from insect cells.
Li J, Chian RJ, Ay I, Celia SA, Kashi BB, Tamrazian E, Matthews JC, Remington MP, Pepinsky RB, Fishman PS, Brown RH Jr, Francis JW.
Li J, et al. Among authors: chian rj.
Biochem Biophys Res Commun. 2009 Jul 31;385(3):380-4. doi: 10.1016/j.bbrc.2009.05.079. Epub 2009 May 22.
Biochem Biophys Res Commun. 2009.
PMID: 19465006
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Insect GDNF:TTC fusion protein improves delivery of GDNF to mouse CNS.
Li J, Chian RJ, Ay I, Kashi BB, Celia SA, Tamrazian E, Pepinsky RB, Fishman PS, Brown RH Jr, Francis JW.
Li J, et al. Among authors: chian rj.
Biochem Biophys Res Commun. 2009 Dec 18;390(3):947-51. doi: 10.1016/j.bbrc.2009.10.083. Epub 2009 Oct 21.
Biochem Biophys Res Commun. 2009.
PMID: 19852934
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Identification of rare protein disulfide isomerase gene variants in amyotrophic lateral sclerosis patients.
Gonzalez-Perez P, Woehlbier U, Chian RJ, Sapp P, Rouleau GA, Leblond CS, Daoud H, Dion PA, Landers JE, Hetz C, Brown RH.
Gonzalez-Perez P, et al. Among authors: chian rj.
Gene. 2015 Jul 25;566(2):158-65. doi: 10.1016/j.gene.2015.04.035. Epub 2015 Apr 22.
Gene. 2015.
PMID: 25913742
Free PMC article.
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Association of UBQLN1 mutation with Brown-Vialetto-Van Laere syndrome but not typical ALS.
González-Pérez P, Lu Y, Chian RJ, Sapp PC, Tanzi RE, Bertram L, McKenna-Yasek D, Gao FB, Brown RH Jr.
González-Pérez P, et al. Among authors: chian rj.
Neurobiol Dis. 2012 Dec;48(3):391-8. doi: 10.1016/j.nbd.2012.06.018. Epub 2012 Jul 3.
Neurobiol Dis. 2012.
PMID: 22766032
Free PMC article.
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Amyotrophic lateral sclerosis-linked FUS/TLS alters stress granule assembly and dynamics.
Baron DM, Kaushansky LJ, Ward CL, Sama RR, Chian RJ, Boggio KJ, Quaresma AJ, Nickerson JA, Bosco DA.
Baron DM, et al. Among authors: chian rj.
Mol Neurodegener. 2013 Aug 31;8:30. doi: 10.1186/1750-1326-8-30.
Mol Neurodegener. 2013.
PMID: 24090136
Free PMC article.
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