Pathogenic p62/SQSTM1 mutations impair energy metabolism through limitation of mitochondrial substrates.
Bartolome F, Esteras N, Martin-Requero A, Boutoleau-Bretonniere C, Vercelletto M, Gabelle A, Le Ber I, Honda T, Dinkova-Kostova AT, Hardy J, Carro E, Abramov AY.
Bartolome F, et al.
Sci Rep. 2017 May 10;7(1):1666. doi: 10.1038/s41598-017-01678-4.
Sci Rep. 2017.
PMID: 28490746
Free PMC article.