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Year | Number of Results |
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2013 | 1 |
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2018 | 1 |
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Systemic ceramide accumulation leads to severe and varied pathological consequences.
EMBO Mol Med. 2013 Jun;5(6):827-42. doi: 10.1002/emmm.201202301. Epub 2013 May 16.
EMBO Mol Med. 2013.
PMID: 23681708
Free PMC article.
Chronic lung injury and impaired pulmonary function in a mouse model of acid ceramidase deficiency.
Yu FPS, Islam D, Sikora J, Dworski S, Gurka J, López-Vásquez L, Liu M, Kuebler WM, Levade T, Zhang H, Medin JA.
Yu FPS, et al.
Am J Physiol Lung Cell Mol Physiol. 2018 Mar 1;314(3):L406-L420. doi: 10.1152/ajplung.00223.2017. Epub 2017 Nov 22.
Am J Physiol Lung Cell Mol Physiol. 2018.
PMID: 29167126
Free PMC article.
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Acid Ceramidase Deficiency is characterized by a unique plasma cytokine and ceramide profile that is altered by therapy.
Dworski S, Lu P, Khan A, Maranda B, Mitchell JJ, Parini R, Di Rocco M, Hugle B, Yoshimitsu M, Magnusson B, Makay B, Arslan N, Guelbert N, Ehlert K, Jarisch A, Gardner-Medwin J, Dagher R, Terreri MT, Lorenco CM, Barillas-Arias L, Tanpaiboon P, Solyom A, Norris JS, He X, Schuchman EH, Levade T, Medin JA.
Dworski S, et al.
Biochim Biophys Acta Mol Basis Dis. 2017 Feb;1863(2):386-394. doi: 10.1016/j.bbadis.2016.11.031. Epub 2016 Dec 1.
Biochim Biophys Acta Mol Basis Dis. 2017.
PMID: 27915031
Free PMC article.
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Markedly perturbed hematopoiesis in acid ceramidase deficient mice.
Dworski S, Berger A, Furlonger C, Moreau JM, Yoshimitsu M, Trentadue J, Au BC, Paige CJ, Medin JA.
Dworski S, et al.
Haematologica. 2015 May;100(5):e162-5. doi: 10.3324/haematol.2014.108530. Epub 2015 Feb 14.
Haematologica. 2015.
PMID: 25682603
Free PMC article.
No abstract available.
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Acid Ceramidase Deficiency in Mice Results in a Broad Range of Central Nervous System Abnormalities.
Sikora J, Dworski S, Jones EE, Kamani MA, Micsenyi MC, Sawada T, Le Faouder P, Bertrand-Michel J, Dupuy A, Dunn CK, Xuan ICY, Casas J, Fabrias G, Hampson DR, Levade T, Drake RR, Medin JA, Walkley SU.
Sikora J, et al.
Am J Pathol. 2017 Apr;187(4):864-883. doi: 10.1016/j.ajpath.2016.12.005.
Am J Pathol. 2017.
PMID: 28342444
Free PMC article.
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On-tissue localization of ceramides and other sphingolipids by MALDI mass spectrometry imaging.
Jones EE, Dworski S, Canals D, Casas J, Fabrias G, Schoenling D, Levade T, Denlinger C, Hannun YA, Medin JA, Drake RR.
Jones EE, et al.
Anal Chem. 2014 Aug 19;86(16):8303-11. doi: 10.1021/ac501937d. Epub 2014 Aug 8.
Anal Chem. 2014.
PMID: 25072097
Free PMC article.
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