Cochlear implantation in children with Mondini dysplasia: our experience

J Laryngol Otol. 2021 Feb;135(2):125-129. doi: 10.1017/S0022215121000372. Epub 2021 Feb 11.

Abstract

Objective: This study details the intra-operative complications, and compares auditory scales post-implantation of either profoundly deaf young children with radiologically normal inner ears (group A) or children with Mondini dysplasia (group B).

Methods: A retrospective survey was carried out of 338 patients with severe to profound sensorineural hearing loss who underwent cochlear implant surgery from February 2015 to May 2017. Patients were divided into 2 groups of 27 patients each. Both groups were followed up to three years post-implantation.

Results: Cerebrospinal fluid ooze developed in 12 patients, and 2 patients had a cerebrospinal fluid 'gusher', one of which had to be explored within 24 hours. After implant use for one year, both groups had similar speech perception scores.

Conclusion: The cerebrospinal fluid gusher in Mondini dysplasia should be anticipated and adequately managed intra-operatively. This study highlights the tailoring of a post-implantation rehabilitation programme according to individual needs.

Keywords: Cerebrospinal Fluid; Cochlear Implants.

MeSH terms

  • Adult
  • Case-Control Studies
  • Cerebrospinal Fluid Leak / epidemiology*
  • Child
  • Cochlear Implantation / methods*
  • Cochlear Implants / adverse effects
  • Ear, Inner / abnormalities*
  • Ear, Inner / diagnostic imaging
  • Ear, Inner / pathology
  • Ear, Inner / surgery
  • Hearing Loss, Sensorineural / rehabilitation
  • Hearing Loss, Sensorineural / surgery*
  • Humans
  • India / epidemiology
  • Intraoperative Complications / epidemiology*
  • Intraoperative Complications / pathology
  • Male
  • Retrospective Studies
  • Speech Perception / physiology
  • Tomography Scanners, X-Ray Computed