[Dermatofibrosarcoma protuberans of Darier and Ferranda study of 28 cases in adult]

Tunis Med. 2005 Aug;83(8):457-62.
[Article in French]

Abstract

Dermatofibrosarcoma protuberans of Darier and Ferrand is a mesenchymatous skin tumor of intermediate malignant potential, characterised by slow growth, local malignancy and a high rate of recurrence. It is a rare tumor, accounting for approximately 0.1% to 0.18% of all malignant skin tumors. Peak incidence of the disease is between 20 to 40 years of age. We report a retrospective study of 28 cases of dermatofibrosarcoma protuberans. We reviewed the clinical features, histopathological and immunohistochemical aspects of this tumor.

Publication types

  • English Abstract

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Dermatofibrosarcoma* / diagnosis
  • Dermatofibrosarcoma* / pathology
  • Dermatofibrosarcoma* / surgery
  • Female
  • Follow-Up Studies
  • Humans
  • Immunohistochemistry
  • Male
  • Middle Aged
  • Neoplasm Recurrence, Local
  • Prospective Studies
  • Skin / pathology
  • Skin Neoplasms* / diagnosis
  • Skin Neoplasms* / pathology
  • Skin Neoplasms* / surgery
  • Time Factors