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Disturbances in mitochondrial bioenergetics and control quality and unbalanced redox homeostasis in the liver of a mouse model of mucopolysaccharidosis type II.
Mol Cell Biochem. 2024 Mar 18. doi: 10.1007/s11010-024-04952-y. Online ahead of print.
Mol Cell Biochem. 2024.
PMID: 38498105
In Vivo Intracerebral Administration of α-Ketoisocaproic Acid to Neonate Rats Disrupts Brain Redox Homeostasis and Promotes Neuronal Death, Glial Reactivity, and Myelination Injury.
Zemniaçak ÂB, Ribeiro RT, Pinheiro CV, de Azevedo Cunha S, Tavares TQ, Castro ET, Leipnitz G, Wajner M, Amaral AU.
Zemniaçak ÂB, et al.
Mol Neurobiol. 2024 May;61(5):2496-2513. doi: 10.1007/s12035-023-03718-9. Epub 2023 Nov 1.
Mol Neurobiol. 2024.
PMID: 37910283
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Disturbance of mitochondrial functions caused by N-acetylglutamate and N-acetylmethionine in brain of adolescent rats: Potential relevance in aminoacylase 1 deficiency.
Bortoluzzi VT, Ribeiro RT, Zemniaçak ÂB, Cunha SA, Sass JO, Castilho RF, Amaral AU, Wajner M.
Bortoluzzi VT, et al. Among authors: zemniacak ab.
Neurochem Int. 2023 Dec;171:105631. doi: 10.1016/j.neuint.2023.105631. Epub 2023 Oct 16.
Neurochem Int. 2023.
PMID: 37852579
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Disruption of mitochondrial bioenergetics and calcium homeostasis by phytanic acid in the heart: Potential relevance for the cardiomyopathy in Refsum disease.
Zemniaçak ÂB, Roginski AC, Ribeiro RT, Bender JG, Marschner RA, Wajner SM, Wajner M, Amaral AU.
Zemniaçak ÂB, et al.
Biochim Biophys Acta Bioenerg. 2023 Apr 1;1864(2):148961. doi: 10.1016/j.bbabio.2023.148961. Epub 2023 Feb 20.
Biochim Biophys Acta Bioenerg. 2023.
PMID: 36812958
Free article.
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L-2-Hydroxyglutaric Acid Administration to Neonatal Rats Elicits Marked Neurochemical Alterations and Long-Term Neurobehavioral Disabilities Mediated by Oxidative Stress.
Ribeiro RT, Carvalho AVS, Palavro R, Durán-Carabali LE, Zemniaçak ÂB, Amaral AU, Netto CA, Wajner M.
Ribeiro RT, et al. Among authors: zemniacak ab.
Neurotox Res. 2023 Apr;41(2):119-140. doi: 10.1007/s12640-022-00625-0. Epub 2022 Dec 29.
Neurotox Res. 2023.
PMID: 36580261
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Disruption of mitochondrial functions involving mitochondrial permeability transition pore opening caused by maleic acid in rat kidney.
Roginski AC, Zemniaçak ÂB, Marschner RA, Wajner SM, Ribeiro RT, Wajner M, Amaral AU.
Roginski AC, et al. Among authors: zemniacak ab.
J Bioenerg Biomembr. 2022 Aug;54(4):203-213. doi: 10.1007/s10863-022-09945-4. Epub 2022 Jul 29.
J Bioenerg Biomembr. 2022.
PMID: 35902433
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