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Treatment with FRAX486 rescues neurobehavioral and metabolic alterations in a female mouse model of CDKL5 deficiency disorder.
CNS Neurosci Ther. 2022 Nov;28(11):1718-1732. doi: 10.1111/cns.13907. Epub 2022 Aug 6.
CNS Neurosci Ther. 2022.
PMID: 35932179
Free PMC article.
Treatment with a GSK-3β/HDAC Dual Inhibitor Restores Neuronal Survival and Maturation in an In Vitro and In Vivo Model of CDKL5 Deficiency Disorder.
Loi M, Gennaccaro L, Fuchs C, Trazzi S, Medici G, Galvani G, Mottolese N, Tassinari M, Giorgini RR, Milelli A, Ciani E.
Loi M, et al. Among authors: mottolese n.
Int J Mol Sci. 2021 May 31;22(11):5950. doi: 10.3390/ijms22115950.
Int J Mol Sci. 2021.
PMID: 34073043
Free PMC article.
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Inhibition of microglia overactivation restores neuronal survival in a mouse model of CDKL5 deficiency disorder.
Galvani G, Mottolese N, Gennaccaro L, Loi M, Medici G, Tassinari M, Fuchs C, Ciani E, Trazzi S.
Galvani G, et al. Among authors: mottolese n.
J Neuroinflammation. 2021 Jul 8;18(1):155. doi: 10.1186/s12974-021-02204-0.
J Neuroinflammation. 2021.
PMID: 34238328
Free PMC article.
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Luteolin Treatment Ameliorates Brain Development and Behavioral Performance in a Mouse Model of CDKL5 Deficiency Disorder.
Tassinari M, Mottolese N, Galvani G, Ferrara D, Gennaccaro L, Loi M, Medici G, Candini G, Rimondini R, Ciani E, Trazzi S.
Tassinari M, et al. Among authors: mottolese n.
Int J Mol Sci. 2022 Aug 5;23(15):8719. doi: 10.3390/ijms23158719.
Int J Mol Sci. 2022.
PMID: 35955854
Free PMC article.
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Expression of a Secretable, Cell-Penetrating CDKL5 Protein Enhances the Efficacy of Gene Therapy for CDKL5 Deficiency Disorder.
Medici G, Tassinari M, Galvani G, Bastianini S, Gennaccaro L, Loi M, Mottolese N, Alvente S, Berteotti C, Sagona G, Lupori L, Candini G, Baggett HR, Zoccoli G, Giustetto M, Muotri A, Pizzorusso T, Nakai H, Trazzi S, Ciani E.
Medici G, et al. Among authors: mottolese n.
Neurotherapeutics. 2022 Oct;19(6):1886-1904. doi: 10.1007/s13311-022-01295-8. Epub 2022 Sep 15.
Neurotherapeutics. 2022.
PMID: 36109452
Free PMC article.
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Cardiac Functional and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder.
Loi M, Bastianini S, Candini G, Rizzardi N, Medici G, Papa V, Gennaccaro L, Mottolese N, Tassinari M, Uguagliati B, Berteotti C, Martire VL, Zoccoli G, Cenacchi G, Trazzi S, Bergamini C, Ciani E.
Loi M, et al. Among authors: mottolese n.
Int J Mol Sci. 2023 Mar 14;24(6):5552. doi: 10.3390/ijms24065552.
Int J Mol Sci. 2023.
PMID: 36982627
Free PMC article.
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Early-onset brain alterations during postnatal development in a mouse model of CDKL5 deficiency disorder.
Tassinari M, Uguagliati B, Trazzi S, Cerchier CB, Cavina OV, Mottolese N, Loi M, Candini G, Medici G, Ciani E.
Tassinari M, et al. Among authors: mottolese n.
Neurobiol Dis. 2023 Jun 15;182:106146. doi: 10.1016/j.nbd.2023.106146. Epub 2023 May 8.
Neurobiol Dis. 2023.
PMID: 37164289
Free article.
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Voluntary Running Improves Behavioral and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder.
Mottolese N, Uguagliati B, Tassinari M, Cerchier CB, Loi M, Candini G, Rimondini R, Medici G, Trazzi S, Ciani E.
Mottolese N, et al.
Biomolecules. 2023 Sep 15;13(9):1396. doi: 10.3390/biom13091396.
Biomolecules. 2023.
PMID: 37759796
Free PMC article.
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