Absent pulmonary valve syndrome with interrupted aortic arch

C Mignosa; D G Wilson; A Wood; C R Kirk; F Musumeci

doi:10.1016/s0003-4975(98)00379-8

Absent pulmonary valve syndrome with interrupted aortic arch

Ann Thorac Surg. 1998 Jul;66(1):244-6. doi: 10.1016/s0003-4975(98)00379-8.

Authors

C Mignosa¹, D G Wilson, A Wood, C R Kirk, F Musumeci

Affiliation

¹ Congenital Heart Disease Centre, and Department of Radiology, University Hospital of Wales, Cardiff, United Kingdom.

PMID: 9692474
DOI: 10.1016/s0003-4975(98)00379-8

Abstract

A surgically treated case of absent pulmonary valve syndrome associated with type B interrupted aortic arch is presented. The presence of a restrictive ductus arteriosus promoted the development of a collateral circulation between ascending and descending thoracic aorta, allowing the child to remain clinically stable after birth.

Publication types

Case Reports

MeSH terms

Aorta, Thoracic / abnormalities*
Collateral Circulation / physiology
Ductus Arteriosus, Patent / pathology
Ductus Arteriosus, Patent / physiopathology
Heart Septal Defects, Ventricular / pathology
Humans
Infant, Newborn
Male
Pulmonary Artery / abnormalities
Pulmonary Valve / abnormalities*
Pulmonary Valve Insufficiency / pathology
Pulmonary Valve Stenosis / pathology
Syndrome