Copper and ceruloplasmin metabolism in the LEC rat, an animal model for Wilson disease

J Inherit Metab Dis. 1998 Jun;21(3):203-6. doi: 10.1023/a:1005335231153.
No abstract available

MeSH terms

  • Animals
  • Ceruloplasmin / metabolism*
  • Copper / metabolism*
  • Disease Models, Animal
  • Female
  • Golgi Apparatus / metabolism
  • Hepatolenticular Degeneration / metabolism*
  • Humans
  • Liver / metabolism*
  • Rats
  • Rats, Mutant Strains
  • Subcellular Fractions

Substances

  • Copper
  • Ceruloplasmin