Goodpasture's disease and Alport's syndromes

Annu Rev Med. 1996:47:377-86. doi: 10.1146/annurev.med.47.1.377.

Abstract

Goodpasture's, or anti-glomerular basement membrane, disease is an uncommon, usually severe disease caused by autoimmunity to a component of certain basement membranes. Alport's syndrome is an inherited, degenerative disorder that affects specific basement membranes. The two are linked by the involvement of type-IV collagen (basement membrane collagen) in their pathogenesis.

Publication types

  • Review

MeSH terms

  • Anti-Glomerular Basement Membrane Disease / diagnosis*
  • Anti-Glomerular Basement Membrane Disease / pathology
  • Anti-Glomerular Basement Membrane Disease / surgery
  • Basement Membrane / pathology
  • Collagen / analysis
  • Fluorescent Antibody Technique
  • Humans
  • Kidney Glomerulus / pathology
  • Kidney Transplantation / pathology
  • Microscopy, Electron
  • Nephritis, Hereditary / diagnosis*
  • Nephritis, Hereditary / pathology
  • Nephritis, Hereditary / surgery
  • Prognosis

Substances

  • Collagen