Abstract
Goodpasture's, or anti-glomerular basement membrane, disease is an uncommon, usually severe disease caused by autoimmunity to a component of certain basement membranes. Alport's syndrome is an inherited, degenerative disorder that affects specific basement membranes. The two are linked by the involvement of type-IV collagen (basement membrane collagen) in their pathogenesis.
MeSH terms
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Anti-Glomerular Basement Membrane Disease / diagnosis*
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Anti-Glomerular Basement Membrane Disease / pathology
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Anti-Glomerular Basement Membrane Disease / surgery
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Basement Membrane / pathology
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Collagen / analysis
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Fluorescent Antibody Technique
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Humans
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Kidney Glomerulus / pathology
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Kidney Transplantation / pathology
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Microscopy, Electron
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Nephritis, Hereditary / diagnosis*
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Nephritis, Hereditary / pathology
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Nephritis, Hereditary / surgery
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Prognosis