Primary hypergammaglobulinemic purpura associated with IgG2 deficiency. A case report

Clin Exp Rheumatol. 1995 Sep-Oct;13(5):663-5.

Abstract

Hypergammaglobulinemic purpura is a rare disease in children. We report a case of a 12 year-old girl with a history of frequent infections. We found the presence of IgG2 deficiency despite polyclonal hypergammaglobulinemia. An IgG subclass determination should be obtained in every child with polyclonal hypergammaglobulinemia and features of immunodeficiency.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Female
  • Humans
  • Hypergammaglobulinemia / complications*
  • Hypergammaglobulinemia / immunology
  • IgG Deficiency / complications*
  • IgG Deficiency / immunology
  • Immunoglobulin G / blood*
  • Purpura, Hyperglobulinemic / complications*
  • Purpura, Hyperglobulinemic / immunology

Substances

  • Immunoglobulin G