[Clinical features of the genetic variants of alpha-1-proteinase inhibitor]

Postepy Hig Med Dosw. 1993;47(2):125-35.
[Article in Polish]

Abstract

Main variants of alpha-1-proteinase inhibitor are reviewed. Some clinical aspects of alpha-1-proteinase inhibitor deficiency concerned with emphysema, hepatic cirrhosis and panniculitis are discussed.

Publication types

  • English Abstract
  • Review

MeSH terms

  • Emphysema / etiology
  • Humans
  • Liver Cirrhosis / etiology
  • Panniculitis / etiology
  • alpha 1-Antitrypsin / genetics*
  • alpha 1-Antitrypsin Deficiency

Substances

  • alpha 1-Antitrypsin