Hypocomplementemic urticarial vasculitis syndrome with severe systemic manifestations

J Pediatr. 1994 May;124(5 Pt 1):742-4. doi: 10.1016/s0022-3476(05)81367-8.

Abstract

We describe two children with clinical and laboratory features of hypocomplementemic urticarial vasculitis syndrome. Both patients had severe, life-threatening manifestations: rapidly progressive glomerulonephritis (patient 1) and pulmonary hemorrhage (patient 2). We conclude that this syndrome may be a potentially severe multisystem disease.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Child
  • Complement System Proteins / deficiency*
  • Glomerulonephritis / etiology*
  • Hemorrhage / etiology*
  • Humans
  • Lung Diseases / etiology*
  • Male
  • Syndrome
  • Urticaria / complications*
  • Vasculitis / complications*

Substances

  • Complement System Proteins