The authors call attention to the importance of directed clinical examination of the urinary secretion system in children with an abnormal development of the large intestine and anorectal zone. In 23.9% of cases the malformations of the large intestine were associated with anomalies in the development or organs of urinary excretion. The symptoms of associated abnormalities in the anorectal zone and urine excretion ducts are described. A scheme for the examination of such patients is proposed.