No abstract available
MeSH terms
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Acidosis / complications
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Biotin / therapeutic use*
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Carboxy-Lyases / metabolism
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Child, Preschool
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Chromatography, Gas
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Diet Therapy
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Glycine / blood
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Humans
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Isoleucine
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Ketones / urine
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Ligases / metabolism
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Male
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Metabolism, Inborn Errors / drug therapy*
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Phosphotransferases / metabolism
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Propionates / blood*
Substances
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Ketones
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Propionates
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Isoleucine
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Biotin
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Phosphotransferases
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Carboxy-Lyases
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Ligases
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Glycine