A case of paravenous retinochoroidal atrophy was followed over a period of more than 2 years. Rapid progression of the disease was reflected in the deterioration of visual acuity and fields. Electroretinographic recordings revealed reduced photopic and scotopic amplitudes according to the extent of the retinal lesions. In electrooculography virtually no slow and no fast light-induced oscillations could be recorded. These results suggest an involvement of the entire retinal pigment epithelium.