Unicommissural unicuspid aortic valve (UAV) presenting as ascending aortic aneurysm with aortic dissection

Echocardiography. 2024 Apr;41(4):e15819. doi: 10.1111/echo.15819.

Abstract

We herein present an exceptionally rare instance of a unicommissural unicuspid aortic valve (UAV) manifesting with an aneurysmal ascending aorta complicated by a type A aortic dissection .

Keywords: UAV; ascending aortic aneurysm; unicommissural; unicuspid aortic valve.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aneurysm, Ascending Aorta
  • Aorta / abnormalities
  • Aorta / diagnostic imaging
  • Aortic Aneurysm* / complications
  • Aortic Aneurysm* / diagnostic imaging
  • Aortic Dissection* / complications
  • Aortic Dissection* / diagnosis
  • Aortic Dissection* / diagnostic imaging
  • Aortic Valve* / abnormalities
  • Aortic Valve* / diagnostic imaging
  • Diagnosis, Differential
  • Echocardiography / methods
  • Echocardiography, Transesophageal / methods
  • Heart Defects, Congenital / complications
  • Heart Defects, Congenital / diagnostic imaging
  • Heart Valve Diseases / complications
  • Heart Valve Diseases / diagnosis
  • Heart Valve Diseases / diagnostic imaging
  • Humans
  • Male

Supplementary concepts

  • unicuspid aortic valve