Zinner syndrome, a rare congenital anomaly affecting males, is characterized by atresia of the ejaculatory duct, seminal vesicle cysts, and ipsilateral renal agenesis. This case report details a 2-year-old boy successfully treated with laparoscopic excision of a dilated vas deferens and seminal vesicle cyst. The rarity of Zinner syndrome in pediatric patients underscores the importance of understanding its diagnosis and minimally invasive surgical management.
Keywords: Mayer-Rokitansky-Küster-Hauser syndrome; Wolffian duct; Zinner syndrome; mesonephric duct; obstructed hemivagina and ipsilateral renal anomalies syndrome.
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