High-Risk Congenital Heart Disease in Pregnancy

Methodist Debakey Cardiovasc J. 2024 Mar 14;20(2):24-35. doi: 10.14797/mdcvj.1306. eCollection 2024.

Abstract

High-risk congenital heart disease (CHD) in pregnancy presents a complex clinical challenge. With improved medical care and increased survival rates, a growing population of adults with complex CHD are surviving to adulthood, including women of reproductive age. This chapter focuses on risk stratification and management of pregnant women with high-risk CHD, emphasizing the importance of considering both anatomical and physiological complexity. Maternal physiological changes, such as blood volume increase, cardiac output changes, and alterations in vascular resistance, can significantly impact high-risk CHD patients. Management of high-risk CHD in pregnancy necessitates a multidisciplinary approach and individualized care.

Keywords: Fontan circulation; cardiac risk stratification in pregnancy; complex congenital heart disease; cyanotic congenital heart disease; systemic right ventricle.

Publication types

  • Review

MeSH terms

  • Adult
  • Female
  • Heart Defects, Congenital* / diagnostic imaging
  • Heart Defects, Congenital* / epidemiology
  • Hemodynamics
  • Humans
  • Pregnancy
  • Pregnancy Complications, Cardiovascular* / diagnosis
  • Pregnancy Complications, Cardiovascular* / epidemiology
  • Pregnancy Complications, Cardiovascular* / therapy
  • Reproduction