Medical Therapy and Monitoring in Adult Congenital Heart Disease Heart Failure

Abstract

Heart failure (HF) in adult congenital heart disease (ACHD) is an increasingly common problem facing ACHD and advanced heart disease and transplant providers. Patients are highly nuanced, and therapies are poorly studied. Standard HF medications are often used in patients who are not targets of large clinical trials. HF management in this data-free zone requires focused, comprehensive team-based care and close follow-up and communication with patients.

Keywords: Adult congenital heart disease; Eisenmenger syndrome; Follow-up; Fontan; Heart failure; Heart failure therapies; Systemic right ventricle.