[Male pseudohermaphroditism]

Pediatr Med Chir. 1985 Jul-Aug;7(4):481-6.
[Article in Italian]

Abstract

After a brief recall of male sexual differentiation, main features of different etiopathogenetic forms conditioning male pseudohermaphroditism (MPSH) are considered. Procedures for an early and exact identification are illustrated in order to formulate an appropriate prognosis. Hormonal treatment and corrective surgery are discussed; in case of severe malformations, a gender reassignment may be evaluated.

Publication types

  • English Abstract

MeSH terms

  • 3-Oxo-5-alpha-Steroid 4-Dehydrogenase / deficiency
  • Disorders of Sex Development* / classification
  • Disorders of Sex Development* / enzymology
  • Disorders of Sex Development* / metabolism
  • Disorders of Sex Development* / therapy
  • Genotype
  • Gonadal Steroid Hormones / metabolism
  • Humans
  • Male
  • Orchiectomy
  • Receptors, Androgen / metabolism
  • Sex Differentiation
  • Testicular Diseases / metabolism
  • Testosterone / biosynthesis

Substances

  • Gonadal Steroid Hormones
  • Receptors, Androgen
  • Testosterone
  • 3-Oxo-5-alpha-Steroid 4-Dehydrogenase