Ebstein's anomaly: an electrophysiological perspective

Anunay Gupta; Mukund A Prabhu; Robert D Anderson; Srinivas Bv Prasad; Timothy Campbell; Samual Turnbull; Geoffrey Lee; Jonathan R Skinner; Jonathan Kalman; Saurabh Kumar

doi:10.1007/s10840-024-01744-8

Ebstein's anomaly: an electrophysiological perspective

J Interv Card Electrophysiol. 2024 Jan 30. doi: 10.1007/s10840-024-01744-8. Online ahead of print.

Authors

Affiliations

¹ Department of Cardiology, Westmead Hospital, Westmead Applied Research Centre, University of Sydney, Darcy Road, Westmead, Sydney, New South Wales, 2145, Australia.
² Department of Cardiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India.
³ Department of Cardiology, Kasturba Medical College Manipal, Manipal Academy of Higher Education, Manipal, Karnataka, India.
⁴ Department of Cardiology, Royal Melbourne Hospital, University of Melbourne, Parkville, Victoria, Australia.
⁵ Department of Cardiology, Fortis Hospital, Bannerghatta, Bengaluru, India.
⁶ Department of Cardiology, Children's Hospital Westmead, Westmead, New South Wales, Australia.
⁷ Department of Cardiology, Westmead Hospital, Westmead Applied Research Centre, University of Sydney, Darcy Road, Westmead, Sydney, New South Wales, 2145, Australia. saurabh.kumar@sydney.edu.au.

PMID: 38289561
DOI: 10.1007/s10840-024-01744-8

Abstract

Ebstein's anomaly of the tricuspid valve (EA) is an uncommon congenital cardiac malformation. It can present with atrioventricular tachycardia (AVRT), atrioventricular nodal re-entrant tachycardia (AVNRT), atrial arrhythmias, and rarely with ventricular tachycardia. The 12-lead electrocardiogram (ECG) is critically important and often diagnostic even prior to an electrophysiology study (EPS). Due to its complex anatomy, it poses particular challenges for mapping and ablation, even for an experienced electrophysiologist. In this review, we aim to provide insight into the electrophysiological perspective of EA and an in-depth analysis of the various arrhythmias encountered in diverse clinical scenarios.

Keywords: Ablation; Arrhythmia; Ebstein anomaly.

Publication types

Review