Sturge-Weber Syndrome: A Report of a Rare Case

Cureus. 2023 Dec 26;15(12):e51110. doi: 10.7759/cureus.51110. eCollection 2023 Dec.

Abstract

Sturge-Weber Syndrome (SWS) is a rare congenital developmental disorder that arises from the abnormal persistence of the embryonic vascular plexus. The syndrome encompasses hamartomatous malformations that can impact the skin, eyes, and nervous system. The broad array of clinical manifestations and potentially life-threatening complications underscores the crucial and imperative need for an accurate diagnosis. An effective treatment strategy for SWS patients involves a multidisciplinary approach. Dental procedures in these individuals pose challenges due to the potential risk for substantial bleeding during both intra- and postoperative phases. This article aims to document a rare case of Sturge Weber Syndrome in a 21-year-old female patient who presented with seizures, unilateral facial port wine stains, gingival hyperplasia, and intracranial calcifications.

Keywords: gingival hypertrophy; port wine stains; radiographic imaging; sturge-weber syndrome; tram track calcification.

Publication types

  • Case Reports