[A case of neonatal splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon]

M N Yu; G Liu; J Y Cao; A J Liu; L W Shao; L M Huang

doi:10.3760/cma.j.cn112140-20231011-00274

[A case of neonatal splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon]

Zhonghua Er Ke Za Zhi. 2024 Feb 2;62(2):180-182. doi: 10.3760/cma.j.cn112140-20231011-00274.

[Article in Chinese]

Authors

M N Yu¹, G Liu¹, J Y Cao¹, A J Liu², L W Shao², L M Huang¹

Affiliations

¹ Department of Neonatal Surgery, Faculty of Pediatrics, the Seventh Medical Center of People's Liberation Army General Hospital, National Engineering Laboratory for Birth Defects Prevention and Control of Key Technology, Beijing Key Laboratory of Pediatric Organ Failure, Beijing 100700, China.
² Department of Pathology, the Seventh Medical Center of People's Liberation Army General Hospital, Beijing 100700, China.

PMID: 38264821
DOI: 10.3760/cma.j.cn112140-20231011-00274

Abstract

患儿男，出生48 h因“腹胀、腹股沟区皮肤瘀斑33 h”就诊。患儿出生15 h出现腹胀、双侧腹股沟瘀斑，伴贫血及血小板降低，腹部CT提示脾肿大、脾内多发低密度区，腹腔穿刺为血性腹腔积液。手术中见脾脏多个不均质充血区，行脾脏部分切除术并保留约20%脾脏，术后病理提示为卡波西样血管内皮瘤。术后腹腔出血停止，血红蛋白及血小板恢复正常。随访13个月患儿生长发育良好，未出现感染、腹胀及出血表现。.

Publication types

Case Reports

MeSH terms

Hemangioendothelioma*
Humans
Infant, Newborn
Kasabach-Merritt Syndrome*
Sarcoma, Kaposi*

Supplementary concepts

Kaposiform Hemangioendothelioma