IgG4-related pachyleptomeningitis with inflammatory pseudotumor

Koki Suezumi; Taira Uehara; Akihiko Taira; Naoki Akamatsu; Tatsuya Tanaka; Yuichiro Hayashi; Mina Komuta; Takayuki Shiomi; Hiroyuki Murai

doi:10.1016/j.ensci.2023.100490

IgG4-related pachyleptomeningitis with inflammatory pseudotumor

eNeurologicalSci. 2023 Dec 25:34:100490. doi: 10.1016/j.ensci.2023.100490. eCollection 2024 Mar.

Authors

Koki Suezumi¹, Taira Uehara¹, Akihiko Taira¹, Naoki Akamatsu¹, Tatsuya Tanaka², Yuichiro Hayashi³, Mina Komuta³, Takayuki Shiomi³, Hiroyuki Murai¹

Affiliations

¹ Department of Neurology, International University of Health and Welfare, Narita Hospital, Narita, Japan.
² Department of Neurosurgery, International University of Health and Welfare, Narita Hospital, Narita, Japan.
³ Department of Anatomic Pathology, International University of Health and Welfare, Narita Hospital, Narita, Japan.

Abstract

•We report the first case of IgG4-related pachyleptomeningitis.•Our case showed also an inflammatory pseudotumor on the side ipsilateral to the pachyleptomeningitis.•The pachyleptomeningitis is probably due to inflammation from the dural pseudotumor spreading along the adjacent meninges.

Keywords: IgG4-related disease; Inflammatory pseudotumor; Leptomeningitis; Pachymeningitis.