Atypical Cogan's syndrome: A case report

J Fr Ophtalmol. 2024 Jan;47(1):104044. doi: 10.1016/j.jfo.2023.104044. Epub 2024 Jan 8.

Abstract

Cogan's syndrome is a rare autoimmune inflammatory disease, characterized by interstitial keratitis and audio-vestibular signs. The syndrome was first described in 1945 by David G. Cogan. Then, it was only in 1980 when Haynes et al. proposed diagnostic criteria for patients with other symptoms and was qualified as atypical form of Cogan's syndrome. Herein, we report a case of a 28-year-old woman with atypical Cogan's syndrome. The patient was treated with corticosteroids and received a cochlear implant.

Keywords: Cogan's syndrome; Deafness; Surdité; Syndrome de Cogan; Uveitis; Uvéite; Vascularite; Vasculitis.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Apraxias / congenital*
  • Autoimmune Diseases*
  • Cochlear Implants*
  • Cogan Syndrome* / complications
  • Cogan Syndrome* / diagnosis
  • Female
  • Humans
  • Keratitis* / diagnosis
  • Syndrome

Supplementary concepts

  • Apraxia, oculomotor, Cogan type