A case of clinically aggressive EBV-negative ENKTL in a non-Asian female patient

J Hematop. 2023 Mar;16(1):33-38. doi: 10.1007/s12308-023-00529-8. Epub 2023 Jan 19.

Abstract

Background: The patient was a 65-year-old White woman who presented to dermatology with a painless, rapidly growing exophytic nodule on her left upper cheek.

Aims/purpose: In this case report, we aim to demonstrate the difficulty of diagnosing Epstein-Barr virus-negative extranodal NK cell lymphomas given the broad differential of NK cell lymphomas and the rarity of EBV-negative extranodal NK cell lymphoma.

Methods: Immunohistochemical studies confirmed the diagnosis of cutaneous, extranodal NK cell lymphoma. Interestingly, Epstein-Barr virus in situ hybridization was negative, which is unusual for most NK cell lymphomas.

Results/conclusions: In our view, a combination of immunohistochemistry, clonality assessment, sequencing, and flow cytometric studies is required.

Keywords: Differential diagnosis; Epstein–Barr virus; Extranodal NK/T cell lymphoma; Immunohistochemistry; Lymphoproliferative disorders/diagnosis.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aggression
  • Epstein-Barr Virus Infections* / complications
  • Female
  • Herpesvirus 4, Human / genetics
  • Humans
  • Lymphoma, Extranodal NK-T-Cell*
  • Lymphoma, T-Cell, Cutaneous*
  • Neoplasms, Connective Tissue*
  • Skin Neoplasms*