Portal Embolisation as Treatment of Severe Portal Hypertension Due to Idiopathic Intrahepatic Arterioportal Fistula: A Case Report

Anne J Klompenhouwer; Adriaan Moelker; Sarwa D Murad; Caroline M den Hoed; Raoel Maan

doi:10.1016/j.jceh.2023.10.006

Portal Embolisation as Treatment of Severe Portal Hypertension Due to Idiopathic Intrahepatic Arterioportal Fistula: A Case Report

J Clin Exp Hepatol. 2024 Mar-Apr;14(2):101295. doi: 10.1016/j.jceh.2023.10.006. Epub 2023 Oct 20.

Authors

Anne J Klompenhouwer¹, Adriaan Moelker², Sarwa D Murad^{1

3}, Caroline M den Hoed^{1

3}, Raoel Maan^{1

3}

Affiliations

¹ Department of Gastroenterology and Hepatology, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
² Department of Radiology and Nuclear Medicine, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
³ The Erasmus MC Transplant Institute, Rotterdam, The Netherlands.

PMID: 38076444
PMCID: PMC10709512 (available on 2025-03-01)
DOI: 10.1016/j.jceh.2023.10.006

Abstract

Intrahepatic arterioportal fistula (IAPF) is a rare cause of portal hypertension. Treatment is usually aimed at restoring the normal portal hemodynamics by obliterating the shunt. This report describes a case of idiopathic IAPF with severe portal hypertension complicated by portal enteropathy with vomiting, gastrointestinal hemorrhage and sepsis. The patient was successfully treated with portal embolization.

Keywords: embolization; intrahepatic arterioportal fistula; portal hypertension.

Publication types

Case Reports