RFX6 Maintains Gene Expression and Function of Adult Human Islet α-Cells

Diabetes. 2024 Mar 1;73(3):448-460. doi: 10.2337/db23-0483.

Abstract

Mutations in the gene encoding the transcription factor regulatory factor X-box binding 6 (RFX6) are associated with human diabetes. Within pancreatic islets, RFX6 expression is most abundant in islet α-cells, and α-cell RFX6 expression is altered in diabetes. However, the roles of RFX6 in regulating gene expression, glucagon output, and other crucial human adult α-cell functions are not yet understood. We developed a method for selective genetic targeting of human α-cells and assessed RFX6-dependent α-cell function. RFX6 suppression with RNA interference led to impaired α-cell exocytosis and dysregulated glucagon secretion in vitro and in vivo. By contrast, these phenotypes were not observed with RFX6 suppression across all islet cells. Transcriptomics in α-cells revealed RFX6-dependent expression of genes governing nutrient sensing, hormone processing, and secretion, with some of these exclusively expressed in human α-cells. Mapping of RFX6 DNA-binding sites in primary human islet cells identified a subset of direct RFX6 target genes. Together, these data unveil RFX6-dependent genetic targets and mechanisms crucial for regulating adult human α-cell function.

MeSH terms

  • Diabetes Mellitus* / metabolism
  • Gene Expression
  • Glucagon / metabolism
  • Humans
  • Insulin / metabolism
  • Islets of Langerhans* / metabolism
  • Regulatory Factor X Transcription Factors / genetics
  • Regulatory Factor X Transcription Factors / metabolism

Substances

  • Glucagon
  • Regulatory Factor X Transcription Factors
  • Insulin