Malignant Peripheral Nerve Sheath Tumor, a rare Intraosseous Malignancy in the Mandible of a Patient with Neurofibromatosis Type 1: A Case Report

Omid Soltaninia; Arash Dehghan; Faryad Fatehi; Hamid Naderi

doi:10.1007/s12070-023-03885-0

Malignant Peripheral Nerve Sheath Tumor, a rare Intraosseous Malignancy in the Mandible of a Patient with Neurofibromatosis Type 1: A Case Report

Indian J Otolaryngol Head Neck Surg. 2023 Dec;75(4):3839-3842. doi: 10.1007/s12070-023-03885-0. Epub 2023 May 20.

Authors

Omid Soltaninia¹, Arash Dehghan², Faryad Fatehi¹, Hamid Naderi¹

Affiliations

¹ Department of Oral & Maxillofacial Surgery, School of Dentistry, Hamadan University of Medical Sciences, Hamadan, Iran.
² Department of Pathology, School of Medicine, Hamadan University of Medical Sciences, Hamadan, Iran.

PMID: 37974847
PMCID: PMC10645782 (available on 2024-12-01)
DOI: 10.1007/s12070-023-03885-0

Abstract

Malignant peripheral nerve sheath tumor (MPNST) is a rare malignancy of nervous tissue. The oral incidence of this lesion is extremely low. MPNST can occur sporadically or in association with neurofibromatosis. We report a rare intraosseous MPNST in the mandible of a 33-year-old female patient with neurofibromatosis type 1.

Keywords: Intraosseous; Malignant peripheral nerve sheath tumor; Neurofibromatosis type 1.

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