Submucosal dissection to close wide cleft palate with folded mucoperiosteum for bilateral cleft lip and palate with popliteal pterygium syndrome

Shinji Kobayashi; Yuichiro Yabuki; Madoka Sugiyama; Takashi Hirakawa; Kenji Kurosawa

doi:10.1093/jscr/rjad575

Submucosal dissection to close wide cleft palate with folded mucoperiosteum for bilateral cleft lip and palate with popliteal pterygium syndrome

J Surg Case Rep. 2023 Oct 21;2023(10):rjad575. doi: 10.1093/jscr/rjad575. eCollection 2023 Oct.

Authors

Shinji Kobayashi¹, Yuichiro Yabuki¹, Madoka Sugiyama¹, Takashi Hirakawa², Kenji Kurosawa³

Affiliations

¹ Department of Plastic and Reconstructive Surgery, Kanagawa Children's Medical Center, Mutsukawa 2-138-4, Minami-ku, Yokohama 232-8555, Kanagawa, Japan.
² Hirakawa Orthodontic Clinic, Kinkoutyou 5-36, Kanagawa-ku, Yokohama 221-0056, Kanagawa, Japan.
³ Department of Genetics, Kanagawa Children's Medical Center, Mutsukawa 2-138-4, Minami-ku, Yokohama 232-8555, Kanagawa, Japan.

Abstract

Characteristic features of popliteal pterygium syndrome (PPS) associated with the craniofacial region include cleft palate, syngnathia, and difficulty with reconstruction. We developed a new procedure of submucosal dissection with periosteotomy to close the folded mucosa in bilateral cleft lip and palate patients with PPS. This technique could be applicable for patients with wide cleft palate.

Keywords: bilateral cleft palate; popliteal pterygium syndrome; submucosal dissection.