Preoperative Nasobiliary Drainage as a Predictor of Response Before Surgical Fistula Creation in Joubert Syndrome With Refractory Cholestatic Pruritis

Maya Biermann; Preeyanka Rubiana Sundar; Hima Veeramachaneni; Field Willingham

doi:10.14309/crj.0000000000001171

Preoperative Nasobiliary Drainage as a Predictor of Response Before Surgical Fistula Creation in Joubert Syndrome With Refractory Cholestatic Pruritis

ACG Case Rep J. 2023 Oct 3;10(10):e01171. doi: 10.14309/crj.0000000000001171. eCollection 2023 Oct.

Authors

Maya Biermann¹, Preeyanka Rubiana Sundar², Hima Veeramachaneni², Field Willingham²

Affiliations

¹ Department of Medicine, Emory University School of Medicine, Atlanta, GA.
² Division of Digestive Diseases, Department of Medicine, Emory University School of Medicine, Atlanta, GA.

Abstract

Cholestatic pruritus is a debilitating symptom associated with many liver diseases and is often refractory to medical management. Nasobiliary drainage is a relatively safe and effective method for treating intractable cholestatic pruritus. It should be considered for patients with refractory cholestatic pruritus who have failed or have contraindications to medical therapy as a predictor of response before surgical fistula creation.

Keywords: Joubert syndrome; nasobiliary drainage; pruritus.

Publication types

Case Reports