The Management of Pyromelic Polymelia in a Low-resource Setting: A Case Report

J Orthop Case Rep. 2023 Sep;13(9):57-60. doi: 10.13107/jocr.2023.v13.i09.3876.

Abstract

Introduction: Polymelia is the presence of supernumerary limbs attached to a segment of the body. It occurs in about 6/10,000 live births with 1.1/10,000 cases involving the lower limbs. It has a heterogeneous pathogenesis including incomplete separation of monozygotic twins.

Case report: A 5-month-old baby with polymelia associated with ectopic right kidney, anorectal agenesis with a rectovaginal fistula, and right corneal opacity, delivered through cesarean section at 37 weeks, 3-day gestation to a 38-year-old mother. There were no known predisposing factors.

Conclusion: In the management of polymelia, a thorough clinical and radiological assessment to identify additional anomalies is critical, and early surgical intervention is safe and optimizes survival.

Keywords: APGAR score; Polymelia; pyromelia.

Publication types

  • Case Reports