Non-Syndromic Sensorineural Hearing Loss in Children

Neuroimaging Clin N Am. 2023 Nov;33(4):531-542. doi: 10.1016/j.nic.2023.05.005. Epub 2023 Jul 11.

Abstract

Pediatric hearing loss is common with significant consequences in terms of language, communication, social and emotional development, and academic advancement. Radiological imaging provides useful information regarding hearing loss etiology, prognosis, therapeutic options, and potential surgical pitfalls. This review provides an overview of temporal bone imaging protocols, an outline of the classification of inner ear anomalies associated with sensorineural hearing loss and illustrates some of the more frequently encountered and/or important causes of non-syndromic hearing loss.

Keywords: Cytomegalovirus infection; Enlarged vestibular aqueduct; Hearing loss; Inner ear malformation; Labyrinthitis; Non-syndromic hearing loss; Sensorineural hearing loss; Temporal bone.

Publication types

  • Review

MeSH terms

  • Child
  • Deafness*
  • Hearing Loss, Sensorineural* / diagnostic imaging
  • Humans
  • Language
  • Temporal Bone / diagnostic imaging