Alveolar soft part sarcoma of the uterine corpus: A 13-year follow-up case report and review of the literature

Szu-Wei Huang; Hsuan-Ying Huang; Hao Lin

doi:10.1016/j.tjog.2023.07.025

Alveolar soft part sarcoma of the uterine corpus: A 13-year follow-up case report and review of the literature

Taiwan J Obstet Gynecol. 2023 Sep;62(5):769-773. doi: 10.1016/j.tjog.2023.07.025.

Authors

Szu-Wei Huang¹, Hsuan-Ying Huang², Hao Lin³

Affiliations

¹ Department of Obstetrics and Gynecology, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University College of Medicine, Kaohsiung, Taiwan.
² Department of Anatomic Pathology, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University College of Medicine, Kaohsiung, Taiwan.
³ Department of Obstetrics and Gynecology, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University College of Medicine, Kaohsiung, Taiwan. Electronic address: haolin@adm.cgmh.org.tw.

PMID: 37679012
DOI: 10.1016/j.tjog.2023.07.025

Abstract

Objective: Female genital alveolar soft part sarcoma (ASPS) is rare and has a favourable prognosis compared to ASPS from other sites. We reported our experience to manage a case with uterine corpus ASPS (UC ASPS) and conducted a literature review on prognosis of ASPS from different sites of female genital tract.

Case report: This report represented a 33-year-old woman who had UC ASPS. She received tumor excision with uterine preservation and had the longest follow-up time (155 months) without recurrence in the literature.

Conclusion: UC ASPS has better prognosis than ASPS from the uterine cervix, the low uterine segment, vulvovaginal area and perineum. We recommended conservative treatment for young women with UC ASPS.

Keywords: Alveolar soft part sarcoma; Female genital tract; Prognosis; TFE3; Uterine corpus.

Publication types

Review
Case Reports

MeSH terms

Adult
Conservative Treatment
Female
Follow-Up Studies
Humans
Perineum
Sarcoma, Alveolar Soft Part* / diagnosis
Sarcoma, Alveolar Soft Part* / surgery
Uterus