A Rare Presentation of Wegener's Granulomatosis in ENT

Indian J Otolaryngol Head Neck Surg. 2023 Sep;75(3):2363-2366. doi: 10.1007/s12070-023-03653-0. Epub 2023 Mar 22.

Abstract

Wegener's granulomatosis or Granulomatosis with polyangiitis is a rare multisystem autoimmune vasculitis disease which may become life threatening due to the various system involvement. Granular hyperplastic gingivitis, the so called "strawberry gingivitis" is a rare manifestation of this disease, yet pathognomic when present. Early diagnosis and treatment is very important.

Keywords: Biopsy; C ANCA; Strawberry gingivitis; Vasculitis; Wegener’s granulomatosis.