[Intraosseous primary clear cell sarcoma misdiagnosed as malignant melanoma: report of a case]

Zhonghua Bing Li Xue Za Zhi. 2023 Aug 8;52(8):868-870. doi: 10.3760/cma.j.cn112151-20221201-01015.
[Article in Chinese]

Abstract

透明细胞肉瘤(clear cell sarcoma,CCS)是一种少见的恶性间叶性肿瘤,占所有软组织肉瘤的1%,常发生于足踝关节深部,与肌腱和腱膜相关,原发于骨内的CCS极其罕见。由于CCS组织形态多样,且与黑色素瘤具有相似的组织学和免疫组织化学特性,因此极易与黑色素瘤混淆。本文报道1例误诊为黑色素瘤的骨内原发性CCS,介绍其临床表现、影像学检查、组织学特征、细胞遗传学及其鉴别诊断要点。.

Publication types

  • Case Reports

MeSH terms

  • Diagnostic Errors
  • Humans
  • Melanoma* / diagnosis
  • Melanoma* / pathology
  • Melanoma, Cutaneous Malignant
  • Sarcoma, Clear Cell* / diagnosis
  • Sarcoma, Clear Cell* / pathology
  • Skin Neoplasms* / diagnosis
  • Skin Neoplasms* / pathology
  • Soft Tissue Neoplasms*