IgG4-related hypertrophic pachymeningitis with chronic subdural haematoma

Pract Neurol. 2023 Oct;23(5):441-445. doi: 10.1136/pn-2023-003750. Epub 2023 Jul 17.

Abstract

Hypertrophic pachymeningitis is a rare disorder of the dura mater of the spine or brain. It can be caused by inflammatory, infective or neoplastic conditions or can be idiopathic. We report a man with hypertrophic pachymeningitis and bilateral chronic subdural haematoma caused by IgG4-related disease. We highlight the diagnostic challenges and discuss possible underlying mechanisms of subdural haematoma formation in inflammatory conditions. Isolated IgG4-related hypertrophic pachymeningitis with chronic subdural haematoma is very rare; previously reported cases have suggested a possible predilection for men in their sixth decade, presenting with headache as the dominant symptom. Given the rarity and complexity of the condition, it should be managed in a multidisciplinary team setting.

Keywords: NEUROIMMUNOLOGY; NEUROPATHOLOGY; NEURORADIOLOGY.

MeSH terms

  • Dura Mater / diagnostic imaging
  • Hematoma, Subdural, Chronic* / complications
  • Hematoma, Subdural, Chronic* / diagnostic imaging
  • Humans
  • Hypertrophy / complications
  • Hypertrophy / diagnosis
  • Immunoglobulin G
  • Magnetic Resonance Imaging / adverse effects
  • Male
  • Meningitis* / complications
  • Meningitis* / diagnostic imaging

Substances

  • Immunoglobulin G