Unilateral Internal Jugular Vein Thrombosis Revealing Behçet's Disease: Through the Eyes of the Ophthalmologist

Neuroophthalmology. 2023 Jan 31;47(3):153-155. doi: 10.1080/01658107.2023.2168016. eCollection 2023.

Abstract

Behçet's disease (BD) is a rare autoimmune disease with an unknown aetiology. It is mostly found in the ancient "silk route" (from the Mediterranean region to the Far East). BD is a vasculitis that can involve veins and arteries of all sizes. Clinical features are dominated by oral and genital aphthous ulcers and uveitis. Central nervous system manifestations include parenchymal (80%) and non-parenchymal involvement (20%). Non-parenchymal forms can include cerebral venous thrombosis. Treatment is based on anti-inflammatory, immunosuppressive and anticoagulant agents, but it remains controversial. We report a rare case of a unilateral jugular being thrombosis revealing BD in a young Moroccan male. He was admitted due to neuro-ophthalmological manifestations (diplopia, and bilateral papilloedema). A good outcome occurred after treatment with anti-inflammatory drugs and anti-coagulation.

Keywords: Behçet; anticoagulation; immunosuppression; jugular vein; multiple thrombosis.

Publication types

  • Case Reports

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