Superficial CD34 fibroblastic tumors and PRDM10-rearranged soft tissue neoplasm: An evolving diagnosis

J Cutan Pathol. 2024 Jan;51(1):11-14. doi: 10.1111/cup.14443. Epub 2023 May 7.

Abstract

Superficial CD34 fibroblastic tumors (SCD34FT) and PRDM10-rearranged tumors (PRTs) are mesenchymal tumors that have recently received increased scientific attention due to their irrefutable similarities yet debatable relationship. A 74-year-old male presented to the dermatology clinic with a violaceous, well-defined nodule on the left medial knee of 2-year duration. Shave biopsy demonstrated spindle cells arranged in a vaguely storiform pattern forming fascicles. Immunohistochemical stains were positive for vimentin, CD68, CD10, and CD34 diffusely. ERG, S-100, HMB45, and SOX-10 were negative. Molecular studies identified a mediator complex subunit 12 (MED12)-PR/SET Domain 10 (PRDM10) gene fusion thus favoring confirming the diagnosis of a PRT. Our patient underwent wide local excision with negative margins and had no complications. This case aims to provide context for considering SCD34FT and PRT as intersecting entities and to discuss a diagnostic approach when encountering these tumors.

Keywords: PRDM10; sarcoma; soft tissue neoplasm; superficial CD34+ fibroblastic tumor.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antigens, CD34
  • Biomarkers, Tumor / analysis
  • Biomarkers, Tumor / genetics
  • Biopsy
  • DNA-Binding Proteins / genetics
  • Humans
  • Male
  • Neoplasms, Fibrous Tissue*
  • Soft Tissue Neoplasms* / diagnosis
  • Soft Tissue Neoplasms* / genetics
  • Soft Tissue Neoplasms* / pathology
  • Transcription Factors / genetics

Substances

  • Transcription Factors
  • Antigens, CD34
  • Biomarkers, Tumor
  • PRDM10 protein, human
  • DNA-Binding Proteins