Cerebellar Tonsillar Descent Mimicking Chiari Malformation

J Clin Med. 2023 Apr 9;12(8):2786. doi: 10.3390/jcm12082786.

Abstract

Chiari I malformation has been defined as cerebellar tonsillar descent greater than 5 mm below the foramen magnum. Suboccipital decompression remains the mainstay of treatment for symptomatic patients. Other conditions sometimes have imaging features that mimic Chiari I malformation. These patients are at risk of misdiagnosis and mismanagement, including surgery that may be unnecessary or may even worsen the underlying condition. The aim of this study was to analyse a series of Chiari I malformation mimics and identify differentiating imaging features. The mimics are categorised as post-traumatic cranio-cervical junction arachnoiditis, dural band, spontaneous intracranial hypotension, idiopathic intracranial hypertension, and cysts. Better understanding of these conditions will assist with diagnosis and optimal management, including avoiding unnecessary surgery.

Keywords: Chiari I malformation; arachnoiditis; cysts; dural band; idiopathic intracranial hypertension; spontaneous intracranial hypotension; syringomyelia.

Grants and funding

This study was supported by a grant from the Column of Hope.