Intraosseous malignant peripheral nerve sheath tumor at the frontal bone in a child: a rare cause of proptosis

Abstract

We report a nine-year-old male having malignant peripheral nerve sheath tumor (MPNST) of the frontal bone, represented with a twelve-month history of ptosis and proptosis in his right eye and enlarged rapidly in the last three months. Except for slight numbness at his one-third of the right forehead, he had no neurological deficit. The patient's both eyes were having normal eye movements, and he had no visual acuity or field loss. After surgery, we observed the patient with no recurrence for 4 years.

Keywords: Intraosseous tumor; Orbital tumor; Pediatric tumor; Proptosis; Ptosis.