Case report: Reconstruction of the long-gap unilateral absence of right pulmonary artery with contralateral pulmonary artery flap and autologous pericardial graft

Tiange Li; Yunfei Ling; Ziqing Xiong; Qi An

doi:10.3389/fcvm.2023.1071111

Case report: Reconstruction of the long-gap unilateral absence of right pulmonary artery with contralateral pulmonary artery flap and autologous pericardial graft

Front Cardiovasc Med. 2023 Mar 8:10:1071111. doi: 10.3389/fcvm.2023.1071111. eCollection 2023.

Authors

Tiange Li¹, Yunfei Ling¹, Ziqing Xiong¹, Qi An¹

Affiliation

¹ Department of Cardiovascular Surgery, West China Hospital of Sichuan University, Chengdu, China.

Abstract

Unilateral absence of pulmonary artery (UAPA) is a rare type of congenital abnormality that may coexist with other congenital abnormalities or present as an isolated lesion, the latter form can be asymptomatic. Surgical procedure is usually carried out when UAPA was diagnosed with significant symptoms, and the aim of surgery is to restore the pulmonary flow distribution. The right-side UAPA is a considerable challenge for surgeons to process surgery, however, technical description of this type of UAPA are limited. Here we described a rare case of a two-month girl with absence of right pulmonary artery, we presented a technique that reconstructs this long-gap UAPA with contralateral pulmonary artery flap and autologous pericardial graft.

Keywords: cardiovascular surgery; congenital heart defects; reconstruction of pulmonary artery; surgical techinque; unilateral absence of pulmonary artery (UAPA).

Publication types

Case Reports

Grants and funding

This article was funded by 1·3·5 project for disciplines of excellence–Clinical Research Incubation Project, West China Hospital, Sichuan University (No. ZYJC21064)