Churg-Strauss syndrome-associated heart failure and left ventricular thrombosis

ESC Heart Fail. 2023 Jun;10(3):2107-2112. doi: 10.1002/ehf2.14244. Epub 2023 Mar 25.

Abstract

We present a case of a 47-year-old woman with a history of asthma and mononeuritis who presented with shortness of breath and fatigue. Heart failure was diagnosed and echocardiography revealed large floating thrombi attached to the left ventricular walls. Cardiac magnetic resonance imaging showed evidence of myocarditis and angiitis. Blood count revealed eosinophilia. She was diagnosed with eosinophilic granulomatosis with polyangiitis or Churg-Strauss syndrome (CSS) according to recently updated criteria. Medical management with specific aetiology (anticoagulation or immunosuppression) and heart failure treatment resulted in clinical improvement. We further discuss the diagnostic approach of CSS with cardiovascular complications and therapeutic management.

Keywords: Churg-Strauss syndrome; Eosinophilic granulomatosis with polyangiitis; Heart failure; Left ventricular thrombus; Myocarditis.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Churg-Strauss Syndrome* / complications
  • Churg-Strauss Syndrome* / diagnosis
  • Churg-Strauss Syndrome* / drug therapy
  • Echocardiography
  • Eosinophilia* / complications
  • Eosinophilia* / diagnosis
  • Female
  • Granulomatosis with Polyangiitis* / complications
  • Heart Failure* / complications
  • Heart Failure* / etiology
  • Humans
  • Middle Aged
  • Thrombosis* / complications
  • Thrombosis* / diagnosis