Mixed IgM- and IgA-mediated epidermolysis bullosa acquisita associated with IgM-λ paraproteinemia in an 81-year-old woman

Thinh Chau; Joseph Wu; Benjamin Kahn; Christopher Elco; M Peter Marinkovich; Kerri E Rieger; Leslie Robinson-Bostom; Elnaz F Firoz

doi:10.1016/j.jdcr.2023.01.024

Mixed IgM- and IgA-mediated epidermolysis bullosa acquisita associated with IgM-λ paraproteinemia in an 81-year-old woman

JAAD Case Rep. 2023 Feb 4:34:7-9. doi: 10.1016/j.jdcr.2023.01.024. eCollection 2023 Apr.

Authors

Thinh Chau¹, Joseph Wu², Benjamin Kahn¹, Christopher Elco², M Peter Marinkovich^{3

4}, Kerri E Rieger^{3

5}, Leslie Robinson-Bostom¹, Elnaz F Firoz¹

Affiliations

¹ Department of Dermatology, Warren Alpert Medical School of Brown University Providence, Rhode Island.
² Department of Pathology, Warren Alpert Medical School of Brown University Providence, Rhode Island.
³ Department of Dermatology, Stanford University, Palo Alto, California.
⁴ Division of Dermatology, Palo Alto Veteran's Affairs Medical Center, Palo Alto, California.
⁵ Department of Pathology, Stanford University School of Medicine, Palo Alto, California.

No abstract available

Keywords: BMZ, basement membrane zone; DIF, direct immunofluorescence; EBA, epidermolysis bullosa acquisita; IPMN, intraductal papillary mucinous neoplasm; IgA, immunoglobulin A; IgM paraprotein; IgM, immunoglobulin M; LABD, linear IgA bullous dermatosis; MGUS; epidermolysis bullosa acquista; immunobullous; immunofluorescence; paraproteinemia; skin fragility.

Publication types

Case Reports