Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis

Rev Port Cardiol. 2023 Feb;42(2):169.e1-169.e4. doi: 10.1016/j.repc.2022.12.007. Epub 2022 Dec 14.
[Article in English, Portuguese]

Abstract

Inflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years' follow-up the patient underwent a second operation to remove tumoral occurrence in the right atrium, diagnosed as an intimal sarcoma. It cannot be confirmed whether the tumoral recurrence with a different diagnosis (intimal sarcoma) was a progression from the primary tumor or the metachronous appearance of a spontaneous sarcoma.

Keywords: Diagnóstico diferencial; Differential diagnosis; Heart neoplasms; Neoplasias do coração; Neoplastic recurrence; Recorrência neoplásica.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Atrial Appendage*
  • Diagnosis, Differential
  • Female
  • Heart Atria / pathology
  • Heart Neoplasms* / diagnostic imaging
  • Heart Neoplasms* / surgery
  • Humans
  • Sarcoma* / diagnosis
  • Sarcoma* / pathology
  • Sarcoma* / surgery