A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis

Maria Paul; Charu Bamba; Vanya Chugh; Nisha Ravikumar; Jayaram S

doi:10.7759/cureus.30790

A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis

Cureus. 2022 Oct 28;14(10):e30790. doi: 10.7759/cureus.30790. eCollection 2022 Oct.

Authors

Maria Paul¹, Charu Bamba¹, Vanya Chugh¹, Nisha Ravikumar¹, Jayaram S¹

Affiliation

¹ Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Abstract

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder with an absence of pain perception, anhidrosis, heat intolerance, and varying degrees of mental retardation. Though cases of CIPA have innate analgesia, they have been known to have tactile hyperesthesia, thus making anesthesia necessary in case of any surgery. Perioperative complications due to abnormal autonomic functions like bradycardia, hypotension, and hyperthermia are major challenges in the anesthetic management of these cases. Here, we report a case on the anesthetic management of CIPA.

Keywords: anaesthetic complications; analgesia; autonomic dysregulation; cipa; perioperative management.

Publication types

Case Reports